Porphyria and Pseudoporphyria
نویسندگان
چکیده
منابع مشابه
Pseudoporphyria or porphyria cutanea tarda? Diagnostic and treatment difficulties.
Fig. 1. Erosions on the forehead. Fig. 2. Erosions, milia and scarring on the dorsum of the hand. Sir, Porphyria cutanea tarda (PCT) is a vesiculobullous skin disorder of heme biosynthesis in which there is an enzyme defect of uroporphyrinogen decarboxylase (Uro-D), leading to accumulation of porphyrins mainly in urine but also in stool and plasma. Pseudoporphyria is clinically similar to PCT, ...
متن کاملPseudoporphyria induced by hemodialysis
Pseudoporphyria is a condition identical to porphyria cutanea tarda (PCT) on clinical and histological grounds, but without any biochemical porphyrin abnormality. Excessive sunlight and UVA exposure (for example tanning beds), drugs such as: non-steroidal anti-inflammatory drugs, retinoids, antibiotics, diuretics and others are supposed to be etiological factors of pseudoporphyria. Cases of PCT...
متن کاملSuccessful outcome of haemodialysis-induced pseudoporphyria after short-term oral N-acetylcysteine and switch to high-flux technique dialysis.
Pseudoporphyria is a blistering disease with skin fragility and shallow scarring that clinically and histopathologically closely resembles porphyria cutanea tarda. The two conditions can be distinguished by porphyrin levels that typically are elevated in porphyria cutanea tarda, but not or only slightly in pseudoporphyria. Pseudoporphyria can be induced by various medications (e.g. non-steroida...
متن کاملPseudoporphyria in association with Hepatitis C virus infection: A case report
Pseudoporphyria is an uncommon bullous disease with similar clinical and histopathological findings to porphyria cutanea tarda, in the absence of detectable porphyrin elevation. We present a 34-year-old man with clinical and histological findings compatible with porphyria cutanea tarda, whose his urinary uroporphyrin was negative and we concluded that he was a case of pseudoporphyria. Concomita...
متن کاملPseudoporphyria in a haemodialysis patient
A 72-year-old female with end-stage renal disease due to chronic glomerulonephritis had been treated with conventional haemodialysis for 6 years. She was referred three months ago for management of blisters and cutaneous fragility on the dorsa of both hands (Figure 1a and b). The patient denied extensive sun exposure, sun beds, or use of medications other than calcium carbonate, vitamin B compl...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Journal of Investigative Dermatology
سال: 1984
ISSN: 0022-202X
DOI: 10.1111/1523-1747.ep12259984